IgG4-related aortitis mimicking intramural hematoma

Introduction: Acute aortic syndromes (AAS) are life-threatening conditions,and despite advances in imaging techniques, their diagnosisand treatment remain challenging. While intramural hematomais much less common than acute aortic dissection (AD),which is the most common form of AAS, they have similar mortalityrates (1). On the other hand, aortitis may mimic intramuralhematoma (IMH) due to radiologic similarity and, thus, may leadto misdiagnosis and treatment.Here, we describe an IgG4-related aortitis case mimickingintramural hematoma (IMH) due to radiologic image and presentingwith chest pain and severe aortic regurgitation.