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dc.contributor.authorTekin, Bahar
dc.contributor.authorAnsen, Gamze
dc.contributor.authorÖrmeci, Tuğrul
dc.contributor.authorHelvacı Yılmaz, Nesrin
dc.contributor.authorŞakul, Bayram Ufuk
dc.date.accessioned2023-05-24T07:50:49Z
dc.date.available2023-05-24T07:50:49Z
dc.date.issued2023en_US
dc.identifier.citationTekin, B., Ansen, G., Örmeci, T., Helvacı Yılmaz, N. ve Şakul, B. U. (2023). Re-evaluation of the symptoms of Hirayama disease through anatomical perspective. Intractable and Rare Diseases Research, 12(1), 62-66. https://doi.org/10.5582/irdr.2022.01117en_US
dc.identifier.issn2186-3644
dc.identifier.issn2186-361X
dc.identifier.urihttps://doi.org/10.5582/irdr.2022.01117
dc.identifier.urihttps://hdl.handle.net/20.500.12511/10966
dc.description.abstractHirayama disease is a rare disease of the anterior horn motor neuron caused by compression of the cervical spinal cord when the neck is flexed. Cervical myelopathy may accompany the disease. It is characterized by symmetrical or asymmetrical muscle weakness and atrophy of muscles innervated by lower cervical and upper thoracic motor neurons. We recorded two male cases of Hirayama disease between the ages of 15 and 21 based on magnetic resonance imaging (MRI) features obtained from the cervical neutral state and from the flexion position which appeared in the right upper extremity. Loss of strength and atrophy in the right upper extremities was existent in clinical findings of these patients. When MRI was taken in the flexion position, there were dilated veins as hypointense signal void on T2 weighted series in posterior epidural area. The contrast enhancement was seen on these veins. It was observed that the posterior dura was displaced anteriorly and the anterior subarachnoid space was narrow. In cases which show clinical findings such as atrophy and loss of strength, having normal MRI results obtained in the neutral position makes it difficult to diagnose Hirayama Disease. In case of a suspicion of Hirayama disease the diagnosis can be made more easily by MRI taken in the flexion position. These case reports aim to bring Hirayama disease to mind and optimize the management of affected individuals.en_US
dc.language.isoengen_US
dc.publisherInternational Advancement Center for Medicine and Health Research Co., Ltd.en_US
dc.rightsinfo:eu-repo/semantics/openAccessen_US
dc.subjectCervical Myelopathyen_US
dc.subjectHirayamaen_US
dc.subjectJuvenile Spinal Muscular Atrophyen_US
dc.subjectMonomelic Amyotrophyen_US
dc.subjectCervical MRIen_US
dc.titleRe-evaluation of the symptoms of Hirayama disease through anatomical perspectiveen_US
dc.typearticleen_US
dc.relation.ispartofIntractable and Rare Diseases Researchen_US
dc.departmentİstanbul Medipol Üniversitesi, Tıp Fakültesi, Temel Tıp Bilimleri Bölümü, Anatomi Ana Bilim Dalıen_US
dc.departmentİstanbul Medipol Üniversitesi, Sağlık Bilimleri Enstitüsü, Anatomi Ana Bilim Dalıen_US
dc.departmentİstanbul Medipol Üniversitesi, Tıp Fakültesi, Dahili Tıp Bilimleri Bölümü, Radyoloji Ana Bilim Dalıen_US
dc.departmentİstanbul Medipol Üniversitesi, Tıp Fakültesi, Dahili Tıp Bilimleri Bölümü, Nöroloji Ana Bilim Dalıen_US
dc.authorid0000-0002-2522-8090en_US
dc.authorid0000-0001-8488-2394en_US
dc.authorid0000-0001-8532-4917en_US
dc.authorid0000-0001-7566-1063en_US
dc.authorid0000-0002-5539-2342en_US
dc.identifier.volume12en_US
dc.identifier.issue1en_US
dc.identifier.startpage62en_US
dc.identifier.endpage66en_US
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.identifier.doi10.5582/irdr.2022.01117en_US
dc.institutionauthorTekin, Bahar
dc.institutionauthorAnsen, Gamze
dc.institutionauthorÖrmeci, Tuğrul
dc.institutionauthorHelvacı Yılmaz, Nesrin
dc.institutionauthorŞakul, Bayram Ufuk
dc.identifier.wos000941533300009en_US
dc.identifier.scopus2-s2.0-85156205266en_US
dc.identifier.pmid36873670en_US
dc.identifier.scopusqualityQ3en_US


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