New variation of scimitar syndrome with tracheal bronchus, upper lobe agenesis, and ventricular septal defect in a child
Künye
Yurtsever, İ., Yeşilbaş, O., Yozgat, C. Y., Tekin, E. ve Yozgat, Y. (2022). New variation of scimitar syndrome with tracheal bronchus, upper lobe agenesis, and ventricular septal defect in a child. Pediatrics International, 64(1). https://doi.org/10.1111/ped.15029Özet
Scimitar syndrome (SS) is a rare and complex disease charac-terized by cardiovascular and bronchopulmonary malforma-tions. In typical SS, anomalous pulmonary drainage of part orall of the right lung into the inferior vena cava, anomaloussystemic arterial supply of the right lung from either the tho-racic or abdominal aorta, and hypoplasia of the right lungoccur.1Abnormal bronchial anatomy, abnormal diaphragm,hemivertebrae, and genitourinary tract anomalies can alsomanifest in SS.2,3Generally, the symptoms of this syndromeappear 7 months after birth.4According to the literature, therehave been numerous cases where additional features of thetypical syndrome have been reported with Scimitar variants.
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Pediatrics InternationalCilt
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