Successful ablation of coexistent mahaim tachycardia and right posterior accessory pathway in a patient with Ebstein's anomaly
Künye
Gül, E. E., Akdeniz, C. ve Tuzcu, V. (2016). Successful ablation of coexistent mahaim tachycardia and right posterior accessory pathway in a patient with Ebstein's anomaly. Türk Kardiyoloji Derneği Arşivi-Archives Of The Turkish Society Of Cardiology, 44(5), 423-426. https://dx.doi.org/10.5543/tkda.2015.31624Özet
The atriofascicular accessory pathway (AP), known as the Mahaim pathway, is a rare form of pre-excitation, comprising less than 3% of all APs. Mahaim AP is characterized by decremental, anterograde-only conduction, and antidromic tachycardia with left bundle branch morphology. Prevalence of Mahaim AP in Ebstein's anomaly is significantly high. In addition, combination of Wolff-Parkinson-White (WPW) syndrome and Mahaim AP in patients with Ebstein's anomaly has been reported. Presently described is the coexistence of Mahaim AP and manifest WPW syndrome in a patient with Ebstein's anomaly, who was successfully ablated without fluoroscopy. Atriyofasiküler aksesuvar yolak (AY) diğer deyimle Mahaim yolakları preeksitasyonun nadir formu olup aksesuvar yolakların %3’den daha azını oluşturmaktadır. Mahaim aksesuvar yolak dekremental, sadece önedoğru iletisi olan ve sol dal bloklu antidromik taşikardi ile kendini gösterir. Mahaim aksesuvar yolağın Ebstein anomalisindeki prevalansı oldukça yüksektir. Ayrıca Wolf-Parkinson-White (WPW) sendromu ve Mahaim AY birlikteliği Ebstein anomalisinde gösterilmiştir. Bu yazıda, Ebstein anomalisi olan hastada WPW ve Mahaim AY birlikteliğinin floroskopisiz başarılı ablasyonunu sunuyoruz.